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KMID : 1144020160120020092
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Journal of Korean Association for Disability and Oral Health
2016 Volume.12 No. 2 p.92 ~ p.95
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DENTAL CARIES TREATMENT OF A PATIENT WITH BECKWITH-WIEDEMANN SYNDROME : A CASE REPORT
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Heo Seon-Jae
Shin Teo-Jeon
Hyun Hong-Keun
Kim Jung-Wook
Jang Ki-Taeg
Lee Sang-Hoon
Kim Chong-Chul
Kim Young-Jae
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Abstract
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Beckwith-Wiedemann syndrome comprises multiple congenital anomalies with a risk of development of childhood tumors. Macroglossia is the predominent finding in Beckwith-Wiedemann syndrome and other findings include postnatal somatic gigantism, abdominal wall defects, nevus flammeus of the face, congenital heart defects, and cleft palate. The aim of this case presentation is to describe the dental treatment of a child with Beckwith-Wiedemann syndrome.
A 3-year-old boy with Beckwith-Wiedemann syndrome visited to the Seoul National University Dental Hospital for dental evaluation and treatment. Due to the multiple caries and poor cooperation, we planned to perform the dental procedure under general anesthesia. The dental procedure was successfully performed and there was no airway complications after extubation.
This case suggests that general anesthesia may be useful for the patient with uncooperative Beckwith-Wiedemann syndrome, since macroglossia and laryngomalacia may exacerbates airway compromise during dental sedation.
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KEYWORD
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Beckwith-Wiedemann syndrome, Dental treatment, Macroglossia
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